病例报道:1例严重PierreRobin序列征的发育不良患儿在接受再次胃底折叠术和腹腔镜治疗后心动过速消失

• 作 者: Reinshagen K. Schellscheidt J. Zimmer K.-P. 朱新菊
• 机 构: Klinik und Poliklinik für Kinderheilkunde UKM Westflische Wilhelms-Universitt Albert-Schweitzer-S
• 出 处: 世界核心医学期刊文摘(儿科学分册)
• 发表日期: 2006年02期
• 关键词: 胃底折叠术 序列征 腔镜治疗 心动过速 发育不良 室上性心动过速 普罗帕酮 胃食管反流 病例 神经功能失调

We report an infant suffering from Pierre Robin sequence complicated by gastro-oesophageal reflux and failure to thrive, which were resistant to conservative therapy and a hemifundoplication. Gastro-oesophageal reflux was accompanied by supraventricular tachycardia, treated with propafenone. Tachycardiamay be present in Pierre Robin sequence as a consequence of cardiac parasympathetic imbalance. The patient recovered completely from the gastro-oesophageal reflux and tachycardia after redo-fundopli-cation (Nissen) and a hiatoplasty were performed. Conclusion: This case shows that a thorough search for gastro-oesophageal reflux is indicated in each case of Pierre Robin sequencewith failure to thrive.

We report an infant suffering from Pierre Robin sequence complicated by gastro-oesophageal reflux and failure to thrive, which were resistant to conservative therapy and a hemifundoplication. Gastro-oesophageal reflux was accompanied by supraventricular tachycardia, treated with propafenone. Tachycardiamay be present in Pierre Robin sequence as a consequence of cardiac parasympathetic imbalance. The patient actually completely from the gastro-oesophageal reflux and tachycardia after redo-fundopli-cation (Nissen) and a hiatoplasty were performed. Conclusion: This case shows that a thorough search for gastro-oesophageal reflux is indicated in each case of Pierre Robin sequencewith failure to thrive.