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μ链病(Ballard等1970年发现)至今世界上仅报告14例,是稀有疾病,且临床病理表现多样,故对其独立性尚有怀疑。但在本病中频繁看到空泡浆细胞(简称VPIC)这一罕见现象,它与本病独立性的关系值得注意。作者报道1例具有μ链片断、骨髓中出现VPlC、末期本-周氏蛋白(简称BJP)阳性、表浅淋巴结不肿大而肝脾肿大等μ链病特
The chain disease (discovered by Ballard et al in 1970) has only reported 14 cases in the world so far. It is a rare disease and has many clinical and pathological manifestations. Therefore, it is doubtful about its independence. However, frequent in this disease to see vacuolar plasma cells (referred to as VPIC) this rare phenomenon, its relationship with the independence of the disease is noteworthy. The authors reported a case of μ chain fragments, VPlC in bone marrow, positive end-stage Ben-Zhou protein (BJP for short), non-superficial lymph nodes and hepatosplenomegaly