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黑色素斑点一胃肠道多发性息肉症候群(Peutz-Jeghers Syndrome)简称PJS。小儿少见,本科曾收治2例,现报导如下: 病例介绍例1 女,7.5岁,因左下腹部及脐周反复发作性疼痛伴大便带血而人院。8个月时曾有脱肛,2岁时面部出现包素斑,继之手、足、臀部出现类似斑点,家庭成员中无类似病史。体检:面部、唇、双颊粘膜、、手指、足趾、足跖面、足跟及臀部有深褐色至黑色斑点,尤以下唇明显。血红蛋白122g/L红细胞4.1×10~(12)/L钡剂灌肠于横结肠,乙状结肠及降结肠各见一息肉,枣大至核桃大。乙状结肠镜检距肛门16cm处肠管前壁4×3×3cm~3菜花状息肉。于1978年11月间划腹探查,市中见空肠上段,横结肠脾曲,乙状结肠下段多发息肉。切
Peutz-Jeghers syndrome (Peutz-Jeghers Syndrome) is abbreviated as PJS. Uncommon in children, undergraduates have been treated in 2 cases, are reported as follows: Case Introduction Case 1 Female, 7.5 years old, due to left lower abdomen and umbilical recurrent pain associated with fecal blood and hospital. At 8 months, there was a prolapse of the anus. At the age of 2 years, there were facial spots on the face, followed by similar spots on the hands, feet, and buttocks. There was no similar history in the family members. Physical examination: dark brown to black spots on the face, lips, cheeks, cheeks, fingers, toes, ankles, heels, and hips, especially the lower lip. Hemoglobin 122g/L red blood cells 4.1×10 12/L barium enema in the transverse colon, sigmoid colon and descending colon each see a polyp, jujube to walnut large. The sigmoidoscopy was performed at a distance of 16 cm from the anus to the intestine anterior wall 4 x 3 x 3 cm ~ 3 cauliflower polyps. In November 1978, the abdominal exploration was performed. In the city, the upper jejunum, the transverse colon, and the lower segment of the sigmoid colon were found to have polyps. cut