Clinical Characteristics and Gene Mutations of Andersen-Tawil Syndrome in Chinese Families

来源 :The 12th Annual Asian and Oceanian Myology Center (AOMC)Scie | 被引量 : 0次 | 上传用户:xuyaya
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Andersen-Tawil syndrome (ATS) is a rare muscle channelopathy associated with cardiac disturbances and dysmorphic features.Aim To investigate the phenotypes and genotypes of Chinese patients with ATS, so as to differentiate from other muscle channelopathies.Materials and Methods Three Chinese patients from two families clinically manifesting periodic paralysis, cardiac arrhythmia and developmental dysmorphy were ascertained though electrophysiological study and muscle biopsy.Further, mutation analysis for KCNJ2 gene was performed.
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