The use of recombinant FXIII in a major acute bleeding episode of a patient with congenital FXIII de

来源 :The 35th World Congress of the International Society of Hema | 被引量 : 0次 | 上传用户：yuhaolf

【摘要】

：

【作者】

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Zoltan Boda

【机构】

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University of Debrecen Thrombosis and Haemostasis Center

【出处】

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The 35th World Congress of the International Society of Hema

【发表日期】

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2014年5期

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Introduction congenital FXIII deficiency is a rare bleeding disorder with a high risk of spontaneous intracranial haemorrhage.Life-long preventive supplementation is mandatory if FXIII activity is Aim to report the effective use of rFXIII for the treatment of a major bleeding in a patient with severe inherited FXIII-A deficiency.

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The use of recombinant FXIII in a major acute bleeding episode of a patient with congenital FXIII de

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