Classification of pulmonary arterial supply in pulmonary atresia with ventricular septal defect and

• 作 者: YE Zankai Liu Yinglong FAN Xiangming LI Zhiqiang YANGXueyong
• 机 构: Department of Pediatric Cardiology,Capital Medical University affiliated Beijing AnzhenHospital,Beij
• 出 处: 第八届北京五洲国际心血管病会议
• 发表日期: 2014年12期
• 关键词: Pulmonary Atresia VentricualrSrieptal Defect Pulmonary Aterial Supply

　　Objective This study was designed to investigate the classifications of pulmonary arterial supply in 48 pulmonary atresia with ventricular septal defect(PANSD)andtreatment strategies.Methods From April,2012,to October,2013,A total of 48 patients with pulmonary atresia with ventricular septal defect(23 male and 25 female,with age of 0.25-15 (2.30± 3.18)years old,weight 4.5-36.1 (10.95 ±6.39) kg) ,who were undertook operations in our Hospital.All of the patients were scanned with multidetector-row computed tomography(MDCT) and transthoracic echocardiography(TTE), according to the informations,all patients supposed to perform operations were evaluated the origins and the traces of MAPCAs(major systemic-pulmonray collateral arteries) as well as the McGoon ratio and Nakata Index.Results In the 48 cases,the pulmonary arterial supply came from the arterial duct(PDA) in 16 (33%) ,MAPCAs in 14 (29%), PDA coexist with MAPCAs in 18 (38%), the McGoon ratio is 1.21±0.41 and the Nakata index is 129.99±88.26mm2/m2 ; During the peri-operative stage, only two were dead.Proceduresincluding:Unifocalization in 2,Modified Blalock-Taussing shunt in 29, Bidirectional cavopulmonary anastomosis in 13.Modified Blalock-Taussing shunt with Bidirectional cavopulmonary anastomosis in 4.Conclusions Variations are to be found in the site of pulmonary atresia and the morphology of the pulmonoary arterial supply in congenital anomaly of PA/VSD.Generally, combined with MDCT and TTE,surgeons can obtain full-scale information of the specific cardiovascular abnormality and make surgical decisions to manage PA/VSD.