成功治疗1例44d男婴脐疝并肝副叶和胆管闭锁症

• 作 者: Pereira R.M. Sim■es E Silva A.C. Rios Leite V.H. 王一飞
• 机 构: Department of Pediatrics School of Medicine Federal University of Minas Gerais (UFMG) Belo Horizont
• 出 处: 世界核心医学期刊文摘(儿科学分册)
• 发表日期: 2006年04期
• 关键词: 胆管闭锁 副叶 脐疝 肝门肠吻合 腹壁缺损修补 出生后 摘除手术 肝功能检查 体重 病例

We report the second case in literature of a boy with the association of large omphalocele, accessory hepatic lobe, and biliary atresia, and the first successful treatment. The patient was submitted to a surgical treatment at 44 days of life, including Kasai procedure, correction of the remnant abdominal wall defect, and removal of a hepatic accessory lobe. The boy evolved with normalization of hepatic function tests. After 15 years of follow-up, the patient is completely healthy, weights 45 kg, and is 1.64 m tall.

We report the second case in literature of a boy with the association of large omphalocele, accessory hepatic lobe, and biliary atresia, and the first successful treatment. The patient was submitted to a surgical treatment at 44 days of life, including Kasai procedure, correction of the remnant abdominal wall defect, and removal of a hepatic accessory lobe. The boy evolved with normalization of hepatic function tests. After 15 years of follow-up, the patient is completely healthy, weights 45 kg, and is 1.64 m tall.