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朗格汉斯细胞组织细胞增生症(langerhans cell histiocytosis,LCH)是以大量朗格汉斯细胞增生、浸润和肉芽肿形成,伴有数量不等的中性粒细胞、嗜酸性粒细胞、淋巴细胞、浆细胞及多核巨细胞浸润,引起组织破坏,导致器官功能障碍为特征的一组肿瘤性疾病~([1])。LCH儿童多见,发病高峰在1~3岁,男女比例为(1.2~2):1,成人发病率很低~([2])。此病罕见,临床表现多样~([3]),缺乏特异性,极易误诊和漏诊。现收治1例LCH患者,报告如下并进行文
Langerhans cell histiocytosis (langerhans cell histiocytosis, LCH) is a large number of Langerhans cell proliferation, infiltration and granuloma formation, with a varying number of neutrophils, eosinophils, lymphocytes , Plasma cells and multinucleated giant cell infiltration, causing tissue damage, resulting in organ dysfunction characterized by a group of neoplastic disease ~ ([1]). LCH children more common, peak incidence in 1 to 3 years old, male to female ratio (1.2 ~ 2): 1, adult morbidity is very low ~ ([2]). The disease is rare, the clinical manifestations of various ~ ([3]), the lack of specificity, easily misdiagnosed and missed diagnosis. One case of LCH patients are admitted, the report is as follows and the text