论文部分内容阅读
目的提高对软组织多形性透明变性血管扩张性肿瘤(pleomorphic hyanilizing angiectatic tumor of soft parts,PHAT)临床、CT和病理表现的认识。方法结合1例右项部软组织PHAT患者的临床资料和文献复习,详细分析该病的临床表现、CT表现及其病理特征。结果该病临床症状轻微且无特征性;CT表现为边界清楚、呈分叶状的卵圆形肿块,平扫密度不均匀,增强后不均匀强化,强化区域其强化值达血管强化程度。其病理特征为呈簇状分布的扩张性薄壁血管;血管壁、血管周围及瘤细胞之间基质明显透明样变性;分布于血管之间的多形性瘤细胞。结论PHAT是一种低度恶性的软组织肿瘤,CT和病理表现具有明显的特征性。
Objective To improve the clinical, CT and pathological findings of pleomorphic hyanilizing angiectatic tumor of soft parts (PHAT). Methods The clinical data and literature review of one case of soft tissue from the right soft tissue were reviewed to analyze the clinical manifestations, CT findings and pathological features of the disease. Results The clinical symptoms of the disease were mild and non-characteristic. The CT findings showed clear, lobulated oval masses with uneven plain scan density and enhanced non-uniform enhancement. The enhancement values of the enhanced region reached the degree of vascular enhancement. The pathological features of the disease are characterized by the expansion of thin-walled blood vessels in clusters; the matrix of the blood vessels, blood vessels, and tumor cells is obviously hyaline degeneration; pleomorphic tumor cells are distributed between blood vessels. Conclusions PHAT is a kind of low-grade soft tissue tumor. The CT and pathological features have obvious characteristics.