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儿童自身免疫性溶血性负血(AIHA)确两种主要类型:急性型和慢性型。急性型刘皮质类固醇和输血治疗效果较好,而慢性型需长期应用皮质类固醇治疗及免疫抑制剂、脾切除、血浆交换等。在慢性AIHA中,伊文氏综合征即AIHA合并特发性血小板减少性紫癜(ITP)尤为难治。最近已有用大剂量IgG静注治疗ITP的报导,而治疗AIHA则未获成功。根据免疫性溶血性贫血和免疫性血小板减少具有共同病理生理特点的假设,作者将这种疗法成功地应
Children with autoimmune hemolytic negative blood (AIHA) are indeed two main types: acute and chronic type. Acute type of corticosteroid and blood transfusion treatment is better, and long-term need for long-term use of corticosteroids and immunosuppressive agents, splenectomy, plasma exchange. In chronic AIHA, Evans syndrome, AIHA, and idiopathic thrombocytopenic purpura (ITP) are particularly refractory. Recently, there have been reports of treatment of ITP with high-dose IgG intravenously, while treatment of AIHA has not been successful. Based on the hypothesis that immune hemolytic anemia and immune thrombocytopenia have common pathophysiological characteristics, the authors successfully administered this therapy should