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本期为Kugelberg-Welander 病(KW 病)特集,与此病有关的主要论文有5篇。一、Werdnig-Hoffmann 病(WH 病)和KW 病的发病机理(大浜荣作等):这两种病都认为是前角细胞的变性性疾病,通常认为是同一疾病的异型,但KW 病的预后良好,故尸检报告很少,尤其更缺乏关于其前根、周围神经的病理改变的记载,故著者以自己的尸检资料为依据进行探讨。第1例,2岁发病,17岁死亡的进行性肌
This issue is a Kugelberg-Welander disease (KW disease) special feature, and the main papers related to this disease are 5 articles. First, the pathogenesis of Werdnig-Hoffmann disease (WH disease) and KW disease (Ohnobu Ohrong, etc.): Both of these two diseases are considered degenerative disease of anterior horn cells, usually considered to be the same type of disease, but KW disease The prognosis is good, so the autopsy report few, especially the lack of records on the pathological changes of its anterior root and peripheral nerves, so the author to their autopsy data as the basis for discussion. The first case, 2-year-old onset, 17-year-old progressive muscle