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血红蛋白H(HbH)病是a型地中海贫血的一种,多发生于东南亚和西亚地区,国内以广东、福建等沿海地区为多见。本省处于内地,地中海贫血发病率很低,偶见β型地中海贫血的病例报道,但未见a型地中海贫血的病例报告。我们遇到一个家系,报告于下: 患者男,46岁,工人,已婚,汉族,世居郎溪县,患者从1984年1月25日起每日出现寒战,弛张型高热(39℃以上),继之大汗后热退,已2月余。在院外曾先后给予正规的抗疟、抗痨和多种抗生素治疗,均未获效。于同年3月11日转入我院。
Hemoglobin H (HbH) is a type of thalassemia major, occurring mostly in Southeast Asia and West Asia, the country to Guangdong, Fujian and other coastal areas more common. The province is in the Mainland, the incidence of thalassemia is very low, occasionally β-thalassemia cases reported, but no case report of a-thalassemia. We met a pedigree with the following reports: Patient male, 46 years old, worker, married, Han nationality, resident Langxi County, chills, remission fever (39 ° C Above), followed by hot sweat after sweating, more than 2 months. Have been given outside the courtyard formal anti-malaria, anti-tuberculosis and a variety of antibiotic treatment, were ineffective. In March 11 the same year into our hospital.