论文部分内容阅读
本文对９例无神经系统症状的肝豆状核变性患者及年龄相匹配的９例有神经系统症状的此病患者，８例正常对照组脑干听觉诱发电位的检测结果进行了分析，结果表明：无神经系统症状的此病患者组中４例（４４％）异常，主要表现为峰间期（Ⅲ～Ⅴ）／（Ⅰ～Ⅲ）＞１，Ⅴ波潜伏期、Ⅲ～Ⅴ、Ⅰ～Ⅴ波峰间期二耳间差值异常（＞＋３ｓ）。有神经系统症状患者组全部异常（１００％），其异常程度及异常发生率显著大于无神经系统症状患者。说明ＢＡＥＰ检测对无神经系统症状的ＨＬＤ患者有一定的辅助诊断价值，但不如对有神经系统症状的患者显著。
In this paper, 9 cases of Wilson’s disease without neurological symptoms in patients with age-matched 9 patients with neurological symptoms of this disease, 8 cases of normal control group brainstem auditory evoked potential test results were analyzed, the results show : There were 4 patients (44%) with no neurological symptoms in this group. The abnormalities were mainly in the interphase (Ⅲ ~ Ⅴ) / (Ⅰ ~ Ⅲ)> 1, Ⅴ wave latency, Ⅲ ~ Ⅴ, Ⅰ ~ Ⅴ The difference between the two peaks during the peak period was abnormal (> + 3s). Patients with neurological symptoms were all abnormal (100%), and their abnormalities and abnormalities were significantly higher than those without neurological symptoms. BAEP detection of non-neurological symptoms of HLD patients have some diagnostic value, but not as good as patients with neurological symptoms.