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Airway-centered interstitial fibrosis(ACIF),a novelform of diffuse interstitial lung disease (ILD) ofunknown cause,was recently presented.~1 There is no finalconclusion on its property and denomination,and it mightbe a new type of idiopathic interstitial pneumonia(IIP).~1Histopathologically,it was characterized by progressivelobular or small ACIF,and neither similar to any knowncategory of airway disease and ILD,nor similar to knownsubtype of IIP.It showed a poor response tocorticosteroids and poor progrnosis.It has been reportedin Caucasian patients,here,we utilized the termidiopathic airway-centered interstitial fibrosis(IAIF)forthe disease to report 2 Chinese patients,in order toimprove understanding and diagnosis of this disease.
Airway-centered interstitial fibrosis (ACIF), a novel form of diffuse interstitial lung disease (ILD) ofunknown cause, was recently presented. ~ 1 There is no final conclusion on its property and denomination, and it mightbe a new type of idiopathic interstitial pneumonia (IIP ). 1Histopathologically, it was characterized by progressive orbicular or small ACIF, and neither similar to any known category of airway disease and ILD, nor similar to knownsubtype of IIP. It showed a poor response to tocorticosteroids and poor progrnosis. It has been reported in Caucasian patients, here, we utilized the termidiopathic airway-centered interstitial fibrosis (IAIF) forthe disease to report 2 Chinese patients, in order toimprove understanding and diagnosis of this disease.