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患者,女性,19岁。主因皮肤苍白.乏力伴气短反复发作6年入院。给予抗贫血治疗,病情好转,2个月后上述症状再次出现,偶尔吐出一口血痰。拍胸片发现双上肺片状阴影,给予抗结核治疗,不见好转。1988年11月无明显诱因又出现上述症状,仍无发热,再次拍胸片示双侧肺弥漫性改变。查体除眼结膜、口唇苍白外,余均正常。肺通气功能为限制性减退,轻度通气储量不足。残气量占肺总量百分比为中度增高。肺弥散率明显减低。纤维支气管镜检查病理证实为右肺上叶含铁血黄素沉着症。诊断为特发性肺含铁血黄素沉着症。经口服硫唑嘌噙呤(1.5mg/kg,1日2次),好转出院。
Patient, female, 19 years old. Mainly due to pale skin. Shortness of breath with recurrent episodes of recurrent 6-year admission. Given anti-anemia treatment, the condition improved, after 2 months the above symptoms appear again and occasionally spit blood sputum. Patches of chest radiographs were found to have double shadow on the top of the lung, given anti-TB treatment without any improvement. November 1988 no obvious incentive and the above symptoms, there is still no fever, chest X-ray again showed diffuse bilateral changes in the lungs. Physical examination except conjunctiva, pale lips, I was normal. Lung ventilatory function is limited decline, lack of adequate ventilation reserves. The residual volume accounted for a moderate increase in the percentage of total lung volume. Pulmonary dispersion was significantly reduced. Fiberoptic bronchoscopy pathology confirmed as right lung lobe hemosiderosis. Diagnosis of idiopathic pulmonary hemosiderosis. After oral azathioprine purine (1.5mg / kg, 2 times a day), improved discharged.