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先天性多发性关节挛缩症(AMC)是先天性、非进行性疾病。Fisher使用的诊断标准为①在出生时至少存在两个以上不同部位的关节挛缩;②不是进行性的神经疾患,③关节呈纺锤形,周围肌肉萎缩。本症的原因不明,一般认为关节的挛缩状态是在子宫内形成的。发病原因通常认为和向神经性病毒的胎儿感染、羊水少等恶劣的胎内环境,脊髓前角细胞变性,肌韧带发育异常和退化,
Congenital multiple joint contracture (AMC) is a congenital, non-progressive disease. The diagnostic criteria used by Fisher were ① at least two or more different parts of the joint contracture at birth; ② are not progressive neurological disorders; ③ the joint is spindle-shaped and the surrounding muscles atrophy. The cause of this disease is unknown, the general state that the contracture of the joint is formed in the womb. The pathogenesis is generally believed that the fetus and neurogenic virus infection, oligohydramnios and other adverse intrauterine environment, degeneration of the spinal cord anterior horn, muscle ligament dysplasia and degeneration,