论文部分内容阅读
特发性肺纤维化(idiopathic pulmonary fibrosis简称IPF)是以肺间质弥漫性纤维化病变为特征的呼吸系统疾病,由Hamman和Rich在1935年和1944年首先报告,亦称Hamman—Rich综合征。1964年Scating认为,本病的基础病变为肺泡炎,因其病因未明,又称隐源性致纤维化肺泡炎(Cryptogenic fibrsing alveolitis,简称CFA)。本文2例具有长期粉尘作业史的IPF患者曾误诊尘肺,后经病理检查确诊
Idiopathic pulmonary fibrosis (IPF) is a respiratory disease characterized by diffuse fibrotic lesions of the lung, first reported by Hamman and Rich in 1935 and 1944, also known as Hamman-Rich syndrome . 1964 Scating that the underlying disease of this disease is alveolitis, because of its etiology is unknown, also known as cryptogenic fibrosing alveolitis (Cryptogenic fibial alveolitis, CFA for short). In this paper, 2 cases of IPF patients with long-term dust history have been misdiagnosed pneumoconiosis, confirmed by pathological examination