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本文报导了两例以膈肌麻痹为早期症状的运动神经元病的罕见病例。两例均为女性,年龄分别为46岁及68岁。均以呼吸困难数月及急性呼吸衰竭入院。检查除有呼吸衰竭症状外,例1远端肌肉似有轻度萎缩,例2有眼底乳头水肿,出血及脑脊液压力320毫米水柱的颅内压增高征象,其余神经系统均无明显异常。胸部x线例1示二侧膈肌升高,例2一侧膈肌升高。但透视下可见除例1右侧膈肌存在微弱运动外,其余膈肌完全麻痹。例1肌电图检查许多肌肉显示插入电位增强。呈现不完全性干扰象、合并许多交电压
This article reports on two rare cases of motor neuron disease with early symptoms of diaphragmatic paralysis. Both cases were female, aged 46 and 68 respectively. All were admitted to hospital with respiratory distress for several months and acute respiratory failure. In addition to the symptoms of respiratory failure, the distal muscle of Example 1 seems to have mild atrophy. In Case 2, there are ocular papillary edema, hemorrhage and cerebrospinal fluid pressure elevation of 320 mmHc. The other nervous systems showed no obvious abnormalities. Chest x-ray example 1 shows the diaphragm on both sides of the rise, the diaphragm on the side of Example 2 increased. However, under fluoroscopy in addition to the right diaphragm in Example 1 there is weak movement, the rest of the diaphragm completely paralyzed. Example 1 Electromyography Many muscles show increased insertion potentials. Showing incomplete interference like, combined with many AC voltage