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阵发性睡眠性血红蛋白尿症研究近况杨仁池综述郝玉书审校阵发性睡眠性血红蛋白尿症（ＰＮＨ）是一种后天获得性血细胞膜缺陷的克隆性疾病，典型病例以慢性血管内溶血为特征。大多数ＰＮＨ患者异常克隆与残余正常造血并存，使本病的发病机制研究受到限制。已知ＰＮＨ患者红...
Paroxysmal nocturnal hemoglobinuria research Yang Yanchi review Hao Yushu revision Paroxysmal nocturnal hemoglobinuria (PNH) is a clonal disease acquired acquired cell membrane defects, the typical case of chronic intravascular hemolysis is characterized. Abnormal clots in most patients with PNH co-exist with residual normal hematopoiesis, the study of the pathogenesis of this disease is limited. Known PNH patients red ...