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幼年性黄色肉芽肿是非朗格汉斯组织细胞良性增生性疾病 ,主要累及皮肤、累及皮肤以外组织和器官者称系统性幼年性黄色肉芽肿 ,受累器官有皮下组织 ,中枢神经系统 ,肝、脾、肺和肾等 ,大多数损害保持稳定无症状 ,或自行消退 ,部分损害进行性增大压迫重要生命器官和组织 ,致残或致死。仅损害增大影响功能和生命者需积极治疗 ,可采取切除 ,局部使用肾上腺皮质激素 ,全身使用肾上腺皮质激素和抗肿瘤药物 ,使用时必须仔细权衡疗效和药物的毒副作用。
Juvenile yellow granulomatosis is a non-Langerhans cells benign proliferative diseases, mainly involving the skin, involving organizations and organs outside the skin, said systemic juvenile yellow granuloma, affected organs have subcutaneous tissue, the central nervous system, liver, spleen , Lungs and kidneys, most of the damage remained stable and asymptomatic, or spontaneous regression, part of the progressive increase in damage to oppress the vital organs and tissues, disability or lethal. Only damage to increase the function and life of those who need active treatment, can be removed, the use of topical corticosteroids, systemic adrenocorticotropic hormone and antineoplastic drugs, the use must be carefully weighed against the side effects and drug side effects.