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[目的]应用部分性脾动脉栓塞(PSE)治疗儿童遗传性球形红细胞增多症(HS)。[方法]12例患儿均经临床及实验室确诊为遗传性球形红细胞增多症,采用PSE方法治疗,栓塞面积在50%～70%。对全部患者栓塞治疗前、后的临床表现、外周血中血红蛋白、白细胞、血小板计数、免疫功能及脾脏大小进行比较。[结果]PSE术后短时期及2年以内随访,全部病例溶血性贫血症状明显改善,实验室各项指标保持正常。[结论]PSE治疗儿童遗传性球形红细胞增多症(HS)疗效可靠值得推广。
[Objective] To treat partial hereditary spherocytosis (HS) in children with partial splenic arterial embolism (PSE). [Methods] All 12 patients were diagnosed as hereditary polycythemia by clinical and laboratory tests. PSE was used to treat the patients with embolization area of 50% -70%. All patients before and after embolization treatment, clinical manifestations, peripheral blood hemoglobin, white blood cells, platelet count, immune function and spleen size were compared. [Results] Shortly after PSE and follow-up within 2 years, the symptoms of hemolytic anemia in all cases were significantly improved, and all the indexes in the laboratory remained normal. [Conclusion] The therapeutic effect of PSE on children with hereditary spherocytosis (RS) is worthy of promotion.