对1例胆管闭锁患婴行肝门肠吻合修复术获成功

• 作 者: Haber B.A. Erlichman J. Thayu M. 王经纬
• 机 构: Division of Gastroenterology and Nutrition The Children's Hospital of Philadelphia Philadelphia PA
• 出 处: 世界核心医学期刊文摘(儿科学分册)
• 发表日期: 2006年11期
• 关键词: 肝门肠吻合 胆管闭锁 婴行 修复术 肝脏移植 核医学成像 胆汁样 出生后 胆汁淤积 吻合口

We present a case report of a boy with biliary atresia who,after hepatoportoenterostomy performed on day 21 of life, had immediate resolution of cholestasis and remained anicteric until 3.5 months of age. He then abruptly developed acholic stools.Nuclear medicine imaging study showed no excretion. Broadspectrum antibiotics and corticosteroids were administered but did not lead to clinical improvement; a surgical revision of the original anastomosis was undertaken at 4 months of age. At 14 months of age, the child is anicteric and growing well. In this case, successful revision of hepatoportoenterostomy averted the need for liver transplantation.

We present a case report of a boy with biliary atresia who, after hepatoportoenterostomy performed on day 21 of life, had immediate resolution of cholestasis and remained anicteric until 3.5 months of age. He then abruptly developed acholic stools. Nuclear medicine imaging study showed no excretion . Broadspectrum antibiotics and corticosteroids were administered but did not lead to clinical improvement; a surgical revision of the original anastomosis was undertaken at 4 months of age. At 14 months of age, the child is anicteric and well well.. In this case, successful revision of hepatoportoenterostomy averted the need for liver transplantation.