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目的：总结手术纠治右室双出口６７ 例的经验。资料与结果：手术年龄４ 个月～１２ 岁，平均（４ ．９８ ±２ ．９６） 岁；体重４ ．１ ～３６ ．０ｋｇ，平均（１５ ．１３ ±５ ．５４）ｋｇ 。其中伴右室流出道梗阻４８ 例，肺动脉高压１８例，肺动脉瓣闭锁１ 例。１３ 例行姑息手术者无死亡。５４ 例行根治术，其中４ 例又行ＩＩ期根治，６ 例行Ｆｏｎｔａｎ 纠治术；根治手术死亡５ 例，病死率８ ．６２ ％ 。本组总病死率７ ．４６ ％ 。结论：右室双出口伴肺动脉高压者，必须早期手术，防止肺血管病变发生。对肺动脉瓣下型室缺的手术纠治较困难，死亡率高。心内隧道补片方法，术后需定期随访，及时发现左室流出道梗阻，必要时需再次手术解除。
Objective: To summarize the experience of 67 cases of right ventricular double outlet. MATERIALS AND RESULTS: The operative age ranged from 4 months to 12 years, with an average of (4.98 ± 2.96) years and weight 4. 1 ~ 36. 0kg, mean (15.13 ± 5.54) kg. Among them, there were 48 cases of right ventricular outflow tract obstruction, 18 cases of pulmonary hypertension and 1 case of pulmonary valve atresia. 13 cases of palliative surgery without death. Fifty-four patients underwent radical surgery, of which 4 patients underwent second-stage radical operation and 6 underwent Fontan correction. Five patients underwent radical operation and the case-fatality rate was 8. 62%. The total fatality rate in this group 7. 46%. Conclusion: Right ventricular outlet with pulmonary hypertension, must be early surgery to prevent the occurrence of pulmonary vascular disease. Pulmonary valve disease in the absence of surgical treatment of more difficult, high mortality. Intracardiac tunnel patch method, regular follow-up after surgery, timely detection of left ventricular outflow tract obstruction, if necessary, to be released again surgery.