论文部分内容阅读
女,14岁,因反复性以左侧肢体为主的阵发性抽搐发作12年而就诊。检查:右侧颜面三叉神经分布区有大片紫红色血管瘤。颅骨平片见两侧颅腔大小不对称,右侧较小,右颅板增厚,右颞顶后区见散在脑回状钙化及迂曲蜿蜒的双曲状血管钙化。脑血管造影未见异常。 讨论:本病一般认为是胚胎早期在中胚叶和外胚叶结构上的先天性发育缺陷,因其累及相应的皮肤及中枢神经节段,出生时皮肤病灶即很明显,但在不久之后,就有中枢神经系统受累表现。但真正
Female, 14 years old, presented with a 12-year episode of recurrent paroxysmal convulsions on the left limb. Check: the right facial trigeminal nerve distribution area has a large purple hemangioma. Skull plain film see both sides of the cranial cavity size asymmetry, smaller right, thickening of the right cranial board, right posterior temporal parietal see scattered calcified in the brain and tortuous meandering hyperbolic vascular calcification. Cerebral angiography showed no abnormalities. Discussion: The disease is generally considered to be early embryonic congenital defects in the structure of the mesodermal and ectodermal development defects, because it involves the corresponding skin and central nervous segment, the skin lesions at birth is obvious, but in the near future, There is the central nervous system involvement performance. But real