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强直性肌营养不良是累及成人最常见的一种肌营养不良。本病主要的心脏表现是传导障碍,本研究旨在确定心电图预测本病长期予后及临床事件的价值。 53例强直性肌营养不良患者,男性27例,女性26例,平均年龄38±15岁,平均随访6.3±4.0年,随访前均无心脏病史或症状,未用心脏病药物或可能影响心电图的药物。 随访前,15例为轻度强直性肌营养不良,23例为中度,15例为重度。52例为窦性心律,1例为心房纤颤。随访前,I度房室阻滞12例,随访中新发生9例,计21例(39％);随访前右束支阻滞1例,随访中新发生5例,计6例(11％);随访前左束支阻滞5例,随访中新发生9
Myotonic dystrophy is one of the most common muscular dystrophy involving adults. The major cardiac manifestations of this disease are conduction disturbances. This study aimed to determine the value of electrocardiography in predicting the long-term prognosis of this disease and in clinical events. 53 cases of myotonic dystrophy patients, 27 males and 26 females, mean age 38 ± 15 years, with an average follow-up of 6.3 ± 4. 0 years, no history of heart disease or symptoms before follow-up, no heart disease drugs or drugs that may affect the ECG . Before follow-up, 15 patients had mild myotonic dystrophy, 23 were moderate, and 15 were severe. 52 cases of sinus rhythm, 1 case of atrial fibrillation. Before follow-up, I degree atrioventricular block in 12 cases, 9 cases occurred in follow-up, accounting for 21 cases (39%); 1 case of right bundle branch block before follow-up, ); Left bundle branch block in 5 cases before follow-up