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特发性肺含铁血黄素沉着症(简称IPH)是一种少见病。1973～1992年我们误诊14例,为提高对本病的认识,现将其误诊情况分析如下: 临床资料本组14例中男8例,女6例。0～2岁3例,～岁6例,～8岁5例。入院时主要症状及体征:本组患者均有不规则发热、反复发作性咳嗽、中～重度贫血。8例咯血或痰中带血,1例鼻衄,4倒肺部有啰音,5例肺部呼吸音粗糙,11例肝肿大。实验室检查:14例均有血红蛋白降低(35～80g/L(3.5～8g/dl),9例查网织红细胞者均增高(1.8～21.5％),10例骨髓像检查皆呈增生性贫血象。胸片:除1例仅有两肺纹理增加外,其余13
Idiopathic pulmonary hemosiderosis (IPH) is a rare disease. From 1973 to 1992, we misdiagnosed 14 cases. To improve the understanding of this disease, the misdiagnosis situation is analyzed as follows: Clinical data The group of 14 males and 8 females and 6 females. 0 ~ 2 years old in 3 cases, ~ 6 years old, ~ 8 years old in 5 cases. The main symptoms and signs on admission: This group of patients have irregular fever, recurrent cough, moderate to severe anemia. 8 cases of hemoptysis or bloody sputum, 1 case of epistaxis, 4 down the lungs with rales, 5 cases of pulmonary respiratory sounds rough, 11 cases of hepatomegaly. Laboratory tests showed that hemoglobin was decreased in all 14 cases (35 ~ 80g / L (3.5 ~ 8g / dl), all 9 reticulocytes were elevated (1.8 ~ 21.5%) in 10 cases) Elephant chest X-ray: except for 1 case, only two lungs increased, 13 others