颞叶发育不全(附一例尸检报告)

• 作 者: 翁建英
• 出 处: 新疆医学院学报
• 发表日期: 1981年S1期
• 关键词: 发育不全 大脑功能紊乱 先天性异常 水囊瘤 尸检报告 硬膜 发育异常 囊肿 综合症 尸检

颞叶发育不全是一种罕见的先天性异常,过去认为都同时伴有硬膜下囊肿或脑脊液的异常积聚。Robinson提出当颞叶或额叶被脑脊液积聚占据而致发育异常或发育低下时称为“颞叶发育不全综合症”。他分析了文献中的15例都有硬膜下单发或多发水囊瘤。本文作者在一例尸检病人中偶尔发现有一侧颢叶发育不全,但没有发现有囊肿,临床上也没有大脑功能紊乱的表现。

Temporal lobule hypoplasia is a rare congenital anomaly, in the past that are accompanied by anomalous accumulation of subdural cyst or cerebrospinal fluid. Robinson proposed that when the temporal or frontal lobe is occupied by cerebrospinal fluid caused by developmental dysplasia or hypoplasia is called “temporal hypoplasia syndrome.” He analyzed 15 cases of subdural solitary or multiple hydrosarcoma in the literature. In an autopsy patient, the author occasionally found a cataractous hypoplasia, but no cysts were found and no clinical signs of brain dysfunction were found.