论文部分内容阅读
脑三叉神经血管瘤又称Sturge-weber syndrome(简称SWS)。是一种罕见的、散发的、病情渐进性发展的综合征。它的三联征包括:沿三叉神经分布的葡萄酒斑、软脑膜血管瘤及眼部畸形,临床表现为多器官受损,包括癫痫,智力低下及青光眼。近10年来,我院共诊治SWS 7例。现报道如下。临床资料1.一般资料:本组7例,男4例,女3例,初次惊厥年龄<6个月5例,6个月-1岁2例,就诊年龄<6个月4例,6个月-2岁3例。2.临床表现:(1)神经系统表现:7例均以惊厥就诊。4例为局限运动性小发作,表现为一侧肢体(皮肤血管瘤对侧
Brain Trigeminal Hemangioma, also known as Sturge-weber syndrome (referred to as SWS). Is a rare, distributed, progressive disease development syndrome. Its triad includes: wine plaques along the trigeminal nerve distribution, pia mater hemangiomas and ocular deformities, clinical manifestations of multiple organ damage, including epilepsy, mental retardation and glaucoma. In the past 10 years, our hospital treated 7 cases of SWS. Report as follows now. Clinical data 1. General information: The group of 7 patients, 4 males and 3 females, primary convulsion age <6 months in 5 cases, 6 months to 1 year in 2 cases, the treatment age <6 months in 4 cases, 6 Month -2 years old in 3 cases. 2. Clinical manifestations: (1) neurological manifestations: 7 cases were treated with convulsions. 4 cases of localized motility episodes, manifested as one side of the limb (cutaneous hemangiomas contralateral