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目的:探讨噬血细胞综合征患儿的临床特征、治疗及预后。方法:对38例噬血细胞综合征患儿的临床症状、体征、试验检查结果、治疗及预后,进行回顾性总结与分析。结果:38例患儿主要表现为发热、肝脾淋巴结肿大、外周血细胞减少、铁蛋白升高、凝血功能异常;经针对性治疗后,治愈3例,好转20例,疗效不佳自动出院9例,死亡6例。结论:噬血细胞综合征病因复杂,临床表现多种多样,病情凶险,预后较差,早期诊断及治疗对预后十分关键。
Objective: To investigate the clinical features, treatment and prognosis of hemophagocytic syndrome children. Methods: 38 cases of hemophagocytic syndrome in children with clinical symptoms, signs, test results, treatment and prognosis were retrospectively summarized and analyzed. Results: The main manifestations of 38 cases were fever, hepatosplenomegaly, peripheral blood cells decreased, ferritin increased, coagulation abnormalities; after targeted therapy, 3 cases were cured, improved in 20 cases, ineffective discharge automatically 9 Cases, 6 cases of death. Conclusion: The causes of hemophagocytic syndrome are complex, with various clinical manifestations, dangerous conditions and poor prognosis. Early diagnosis and treatment are crucial to prognosis.