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作者经治1例遗传性球形红细胞增多症并发胆石症,行胆石摘除和脾切除术后,临床症状显著改善。病例女,14岁。父及姐妹的周围血象可见球形红细胞。于11岁时出现贫血、黄疸。14岁时因发烧、头痛、恶心、黄疸及向右肩、右腰放散的发作性腹痛及绞痛而入院。营养发育中等,皮肤、球结膜轻度黄疸,面色苍白,睑结膜贫血状,心音纯,肺野清,脾肋下5～6 cm。Hb81g/L(8.1 g/dl),RBC2.47×104/L(2.47×10~4/mm~3),网织红细胞上升到200‰,红细胞大小不等,无中心淡染的小球形红细胞占大半。散见有核红细胞和Jo lly小体。GOT、GPT正常,LDH中度升高,总胆红质、间接胆红质增高,腹痛时总胆红质122.1μmol/L(7.14mg/dl),
The author of a case of hereditary spherocytosis complicated by cholelithiasis, gallstone removal and splenectomy, the clinical symptoms significantly improved. Case female, 14 years old. The peripheral blood of the father and sister shows spherical red blood cells. Aged at the age of 11, jaundice. 14 years old due to fever, headache, nausea, jaundice and to the right shoulder, right back of the spit and the onset of abdominal pain and colic admission. Nutritional development, skin, conjunctival mild jaundice, pale, palpebral conjunctiva anemia, pure heart sounds, clear lung lungs, spleen ribs 5 ~ 6 cm. Hb81g / L (8.1g / dl), RBC2.47 × 104 / L (2.47 × 10 ~ 4 / mm ~ 3), reticulocytes increased to 200 ‰, red blood cell sizes ranging from the center of lightly-stained small spherical red blood cells Accounting for more than half. See the nucleated red blood cells and Jo lly bodies. GOT, normal GPT, moderate elevated LDH, total bilirubin, increased indirect bilirubin, total bilirubin 122.1 μmol / L (7.14 mg / dl)