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韩-薛-柯氏(Hand-Shüller-Christian)综合征为一种发生于儿童的罕见病。韩-薛-柯氏综合征属于组织细胞病的一种中间型,据文献报告,诊断主要依靠骨损、突眼、尿崩三大特征进行诊断,最后由病理活检证实,但临床上三大特征同存者并不多见,故应视作非典型的韩-薛-柯氏综合征。作者于1980年9月经病理检查证实,1例非典型韩-薛-柯氏综合征,兹作一报道。马××,男,16岁,左小腿出现单个肿块和头顶部及右颈部出现多发性肿块3个月,左眼突出一个月,于1980年9月13日入院。查体:颅顶部触及5个蚕豆大及杏子大肿块,右颈部
Hand-Shüller-Christian syndrome is a rare condition that occurs in children. South Korea - Xue - Koch’s syndrome is an intermediate type of histiocytosis, according to the literature report, the diagnosis mainly depends on the three characteristics of bone loss, exophthalmos, diabetes insipidus diagnosis, and finally confirmed by biopsy, but the clinical three Features common with those who are rare, it should be considered atypical Han - Xue - Koch syndrome. The author in September 1980 confirmed by pathology, an atypical Korean - Xue - Koch syndrome, made a report here. Horse × ×, male, 16 years old, a single mass in the left calf and multiple masses in the top and right neck appear for 3 months. The left eye protrudes for one month and is admitted on September 13, 1980. Physical examination: the top of the skull touched 5 broad beans and large apricots, right neck