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遗传性进行性肾炎(Hereditary Progre-ssive Nephritis) 又名遗传性家族性疾病(Alput Syndrome)。临床主要特点为反复血尿,进行性慢性肾功衰竭,部分病人合并耳聋、眼疾。我院儿科自1973年至1984年治疗3例,现总结如下: 例1:男,14周岁.生后健康,4个月始无症状性血尿及蛋白尿(+～++),时轻时重,多次住院诊断不明.多方治疗始终未愈。6岁始晨起双眼脸浮肿,白天活动后消失。8岁始双侧耳鸣耳聋并逐渐加重(高频损失在耳为60分贝,右耳为46.6分贝)。有时高血压(140/90mmHg)。11岁始浮肿转重,呈全身性,必须服用利尿药才能减
Hereditary Progre-ssive Nephritis (also known as hereditary familial disease (Alput Syndrome. The main clinical features of hematuria repeated, progressive chronic renal failure, some patients with deafness, eye disease. Pediatrics in our hospital from 1973 to 1984, the treatment of 3 cases, are summarized as follows: Example 1: male, 14 years old, healthy after birth, 4 months asymptomatic hematuria and proteinuria (+ ~ + +), when light Heavy, multiple inpatient diagnosis is unknown. Multi-treatment has not healed. Eyes edema from the beginning of 6 years old, disappeared during the day activities. Bilateral tinnitus and deafness began to worsen at the age of 8 (high-frequency loss of 60 dB in the ear and 46.6 dB in the right ear). Sometimes high blood pressure (140 / 90mmHg). Edema at the age of 11 turns heavy, was systemic, must take diuretics to reduce