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地中海贫血是一种常染色体的遗传性疾病,是由于一种或几种肽链的合成发生部分或完全抑制所引起的贫血。临床上常见的有α地中海贫血和β地中海贫血。在我国,地中海贫血并不少见。上海、江苏、浙江、四川、广东及广西均有报道,尤以广东的发病率较高。近几年,重型地中海贫血的治疗有了较大的进展,在原有的输血、脾脏切除和铁络合剂三大疗法的基础上,又有一些新的治疗方法和手段在临床上应用,本文就此作一简单的文献复习。
Thalassemia is an autosomal genetic disorder caused by the partial or complete inhibition of anemia caused by the synthesis of one or several peptide chains. Common clinical α-thalassemia and β-thalassemia. In our country, thalassemia is not uncommon. Shanghai, Jiangsu, Zhejiang, Sichuan, Guangdong and Guangxi are all reported, especially in Guangdong. In recent years, great progress has been made in the treatment of thalassemia major. Based on the three major blood transfusion, splenectomy and iron complexing agents, there are some new treatment methods and methods that are clinically applied. Make a simple review of the literature.