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背景/目的:所有的迪乔治综合征都会导致功能型T细胞缺陷。笔者主张在婴幼儿时期对迪乔治综合征患儿实施同种异体胸腺组织移植来重建其免疫功能。这项研究回顾分析了多学科治疗这种复杂患儿的情况。方法:从1991-2001年,笔者评估了患有迪乔治综合征的16例患儿。这些患儿接受了多学科的内科和外科手术治疗。回顾其临床记录。结果:4例患儿因没有接受胸腺移植而死亡,其他12例患儿进行移植术后存活下来。移植时这些婴幼儿的平均年龄是2.7个月(极差1.1-
Background / Aim: All DeGeaux syndrome causes functional T cell defects. The author advocates the implementation of allogeneic thymus transplantation in children with DiGeorge syndrome during infancy to rebuild its immune function. The study reviewed and analyzed the multidisciplinary treatment of this complex child. Methods: From 1991 to 2001, I evaluated 16 children with DeGeorge syndrome. These children received multidisciplinary medical and surgical treatment. Review its clinical records. Results: Four children died of thymus transplantation, and the other 12 children survived the transplant. The average age of these infants at transplantation was 2.7 months (very poor 1.1-