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三尖瓣闭锁为罕见复杂性先心病,我院收治先心病390例中见1例,现报告如下。患者男,14岁,于1986年4月12日入院。患者生后口唇、指甲紫绀,且逐渐加重。家族史无特殊。体检:BP90/75mmHg。发育差,口唇、甲床紫绀明显,指趾杵状。颈静脉怒张,未见搏动。心尖部可触及抬举样搏动,听诊第一心音增强,P_2呈单一音。肝右肋缘下2cm可触及。下肢无浮肿。实验室检查:Hb 20.1
Tricuspid atresia is a rare complex congenital heart disease, congenital heart disease in our hospital for 390 cases, see 1 case, are as follows. The patient, male, 14 years old, was admitted on April 12, 1986. After the patient’s lips, nails cyanosis, and gradually increased. No special family history. Physical examination: BP90 / 75mmHg. Poor development, lips, cyanosis nail bed marked, toe clubbing. Jugular vein engorgement, no beats. Apex can reach the lift-like beating, auscultatory heart sound increased, P_2 was a single tone. 2cm under the right rib margins can be touched. Lower extremity without edema. Laboratory examination: Hb 20.1