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结节性脂膜炎全称回归型发热性非化脓性结节性脂膜炎。又称Weberchristian氏病。临床表现多变,易误诊为风湿性关节炎、结节性多动脉炎、恶性组织细胞病、恶性淋巴瘤、系统性红斑性狼疮、败血症、黑热病、白塞氏病等各种结缔组织疾病。但合并肾脏损害误诊为肾炎者较少见。现将我们所见二例经病理活检证实为全身性结节性脂膜炎并肾脏改变报告如下: 例1、汪某、女性、67岁、患者于21年前分娩后受凉发现双下肢出现黄豆大小
Nodular panniculitis full name regression of febrile non-suppurative nodular peritonitis. Also known as Weberchristian’s disease. Clinical manifestations varied, easily misdiagnosed as rheumatoid arthritis, polyarteritis nodosa, malignant histiocytosis, malignant lymphoma, systemic lupus erythematosus, sepsis, kala-azar, Behcet’s disease and other connective tissue diseases. However, misdiagnosed as kidney neoplasm with renal damage are rare. Now we see two cases confirmed by pathological biopsy of systemic nodular panniculitis and renal changes are reported as follows: Example 1, Wang, female, 67 years old, 21 years ago, patients found cold in both legs appeared after delivery of soybeans size