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目的：了解原发性心内膜弹力纤维增生症（简称心弹）患儿的心内结构及心功能改变的情况及其指导临床诊断、治疗及预后的价值。方法：心弹组随诊患儿２３例（均经地高辛治疗），年龄３～１７（７．２２±４．２０）岁。距初诊时间３年以上，设配对对照组年龄、性别、身长、体重一致的正常儿童２３名。应用Ｍ型超声心动图、二维超声心动图和多普勒彩色超声心动图测量心脏房室腔的大小、心室壁的厚度及运动，各瓣口血流频谱参数及心功能指数。结果：心弹患儿左心房、左心室明显缩小。除一例１４岁患儿心脏恢复正常外，其余仍轻度扩大。左心室收缩功能与对照组仍有差别。结论：心弹患儿经过３年以上的治疗病情明显好转，但左心收缩功能仍较对照组略低，左心亦较对照组大，应坚持长期治疗。
Objective: To investigate the changes of cardiac structure and cardiac function in children with primary endocardial fibroelastosis and its value of guiding clinical diagnosis, treatment and prognosis. Methods: Twenty-three children (all treated with digoxin) were followed up in the heart-beat group, ranging in age from 3 to 17 (7.22 ± 4.20) years. From the initial diagnosis of more than 3 years, with the control group set the age, gender, length, weight of normal children 23. The size of cardiac atrioventricular cavity, the thickness and movement of ventricular wall, the spectral parameters of blood flow in each valve orifice, and cardiac function index were measured by M-mode echocardiography, two-dimensional echocardiography and Doppler color echocardiography. Results: Left atrium and left ventricle were significantly reduced in children with heartbeat. In addition to a 14-year-old children with normal heart return to normal, the rest still slightly expanded. Left ventricular systolic function and the control group are still different. Conclusion: The patients with heart-bouncing syndrome improved significantly after 3 years of treatment. However, left ventricular systolic function was still slightly lower than that of the control group, and left heart was also larger than the control group. Long-term treatment should be adhered to.