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目的探讨成人颅内非典型畸胎瘤样/横纹肌样瘤的影像和病理特征。资料与方法回顾性分析2例经手术病理证实的成人颅内非典型畸胎瘤样/横纹肌样瘤患者MRI资料并文献复习。结果 1例MRI表现类似脑膜瘤征象:实质部分呈等T1、等T2信号,扩散加权成像(DWI)高信号,宽基底与脑膜接触和均匀强化;又有原始神经外胚叶肿瘤(PNET)特点:实性部分呈等T1、等T2伴多房小囊变,DWI高信号;室管膜强化提示脑脊液播散。另1例囊实性病变类似胶质瘤,但实质部分T2接近等信号,有微囊和明显均匀强化,又类似神经节细胞胶质瘤。两例病理均见肌母细胞和细胞丰富能解释等T1、等T2信号和DWI高信号;血管增生明显从而强化显著;灶性坏死易见类似胶质瘤,因此,MRI表现基本能反映病理学变化。结论成人颅内幕上非典型畸胎瘤样/横纹肌样瘤的MRI表现类似于髓母细胞瘤、PNET、恶性胶质瘤及神经节细胞胶质瘤,但成分更混杂、更具中枢神经系统播散潜力为本病特点,发生在幕上、多发可能有助于本病定性诊断,确诊依赖病理组织学检查。
Objective To investigate the imaging and pathological features of adult atypical teratoma / rhabdomyosarcoma. Materials and Methods MRI data and literature reviews of 2 patients with intracranial atypical teratoma / rhabdomyosarcoma confirmed by surgery and pathology were retrospectively reviewed. Results One case showed similar signs of meningioma: the T1, T2, T2, DWI high signals, wide basement and meningeal contacts were uniformly enlarged and the features of primitive neuroectodermal tumor (PNET) : Solid part was equal T1, T2 and other small paroxysmal small cystic change, DWI high signal; ependymal enhanced prompt dissemination of cerebrospinal fluid. Another case of cystic lesions similar to glioma, but the real part of T2 close to other signals, microcapsules and significantly uniform enhancement, and similar ganglion cell glioma. Both cases showed myoblasts and abundant cells, which could explain T1 and other T2 signals and DWI high signals. Vascular hyperplasia was obviously strengthened and focal necrosis was easily seen as glioma. Therefore, MRI findings basically reflected the pathology Variety. Conclusion MRI findings of atypical teratoma / rhabdomyosarcoma in adult patients with intracranial supratentorial intracranial tumors are similar to those of medulloblastoma, PNET, glioblastoma and ganglioneuroblastoma, but the components are more mixed and more CNS-borne Scatter potential for the characteristics of this disease occurs in the curtain, multiple may contribute to the qualitative diagnosis of this disease, the diagnosis depends on histopathological examination.