遗传性球形红细胞增多症(附9例临床分析)

• 作 者: 王玉巧 高熙智
• 机 构: 郯城县高峰头分院,郯城县高峰头分院,
• 出 处: 泰山医学院学报
• 发表日期: 1984年01期
• 关键词: 小球形红细胞 红细胞脆性 红细胞膜 溶血性贫血 急性发作 黄疸 膜收缩蛋白 新生儿期 球形红细胞 肝脾肿大

遗传性球形红细胞增多症(以下简称遗传球),是一种伴有遗传性红细胞膜缺陷的溶血性贫血。临床主要特征有小球形红细胞显著增多,红细胞脆性增高。临床上有不同程度的贫血,黄疸和肝脾肿大,病程较慢但可伴有急性发作。脾切除疗效良好。现将82～83年(在青医附院进修期间)收治的9例报告如下。

Hereditary spherocytosis (hereinafter referred to as genetic ball), is a hereditary erythrocyte membrane defect hemolytic anemia. The main clinical features of small spherical erythrocytes increased significantly increased erythrocyte fragility. There are different degrees of clinical anemia, jaundice and hepatosplenomegaly, slower course but may be accompanied by acute attack. Splenectomy with good effect. Now 82 to 83 years (during the Green Affiliated Hospital training period) were treated 9 cases are as follows.