几种以黄疸为突出表现的综合征

• 作 者: 何子祥
• 出 处: 临床荟萃
• 发表日期: 1988年07期
• 关键词: 综合征 黄疸 结合胆红素 非结合胆红素 胆红素代谢 血清 肝细胞 新生儿 慢性胆道疾病 皮肤痊痒

本文简述几种以黄疸为突出表现的综合征,是一组先天性胆红素代谢缺陷所致的黄疸。临床虽然少见,但与其它类型的黄疸进行鉴别,避免误诊,甚为重要。 这组综合征可分为二大类型: 一、主要由血清非结合胆红素增高所致 (一) Gilbers综合征; (二) Crigler—Najjar综合征;(三) Lucey—Driscoll综合征。 二、由血清结合胆红素增高所致

This article describes several jaundice as a prominent syndrome, is a group of congenital bilirubin metabolism caused by jaundice. Although rare clinical, but with other types of jaundice identification, to avoid misdiagnosis, is very important. This group of syndromes can be divided into two major types: First, mainly due to elevated serum non-conjugated bilirubin (a) Gilbers syndrome; (b) Crigler-Najjar syndrome; (c) Lucey-Driscoll syndrome. Second, due to increased serum bilirubin