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儿童噬血细胞综合征(HPS)是一组以淋巴细胞、巨噬细胞非恶性增生伴噬血细胞增多引起多脏器浸润及全血细胞减少为特征的疾病。患者病情常发展迅速,若不及时诊治预后很差[1]。正确认识该病的临床表现,及时干预是抢救成功的关键。为增加对本病的认识,我们对确诊为儿童HPS的18例患
Child hemophagocytic syndrome (HPS) is a group of diseases characterized by non-malignant proliferation of lymphocytes, macrophages with hemophagocytosis causing multiple organ infiltration and pancytopenia. Patients often develop rapidly, if not timely diagnosis and treatment of poor prognosis [1]. Correct understanding of the clinical manifestations of the disease, timely intervention is the key to the success of the rescue. To increase awareness of the disease, we identified 18 patients diagnosed with HPS in children