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迟发性皮肤卟啉症是一种卟啉代谢障碍性疾病,其特点为暴露部位皮肤发生水疱、粟丘疹、色素沉着、多毛和硬皮病样斑块,尿卟啉排出增多。此病罕见,现报告一例如下。 邓××,男性,29岁,住院号172779,因颜面、颈部、四肢伸侧反复起水疱7年余,此次发作90天,于1981年5月5日入院。患者于1974年10月因口腔溃疡服灰黄霉素,每日600毫克。半月后,双耳廓、颜面及四肢伸侧发生散在红斑及黄豆至指头大小的水疱,疱壁紧张不易破,微痒,愈后遗留浅疤痕,部分色素沉着。
Late-onset cutaneous porphyria is a disorder of metabolic disorder of porphyria characterized by blisters, milia, pigmentation, hirsutism and scleroderma-like plaques on the exposed parts of the skin and increased urinary porphyrin excretion. The disease is rare, a report is as follows. Deng × ×, male, 29 years old, hospital number 172779, due to face, neck, limbs repeatedly blisters blisters more than 7 years, the onset of 90 days, on May 5, 1981 admitted. Patients with griseofulvin oral ulcer in October 1974, 600 mg daily. Half a month later, both ears, face and extensor limbs scattered erythema and soybeans to finger-sized blisters, blister wall tension is not easy to break, itchy, left after the shallow scar, some pigmentation.