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目的探讨儿童降结肠血管周上皮样细胞分化肿瘤的临床特征、影像学和病理学特征,提高对结肠血管周上皮样细胞分化肿瘤的认识。方法对1例儿童降结肠血管周上皮样细胞分化肿瘤的临床表现、影像学表现和病理学特征进行总结。结果该例患儿临床表现为反复血便,影像学表现为富血供肿瘤,免疫组织化学显示肿瘤细胞HMB45弥散强阳性。结论降结肠血管周上皮样细胞分化肿瘤是一种生物学行为未定的间叶源性肿瘤,有其独特的影像学及组织形态及免疫组织化学表型。目前尚无明确的良、恶性诊断标准。以手术完整切除为主要治疗方法,术后密切随访。
Objective To investigate the clinical features, imaging features and pathological features of descending colon pericytes in children and to improve the understanding of differentiated tumors of colonic pericytes in children. Methods The clinical manifestations, imaging features and pathological features of 1 pediatric descending colon pericytes were analyzed. Results The clinical manifestations of this case of children with recurrent bloody stool, imaging showed blood-rich tumor, immunohistochemistry showed strongly diffuse HMB45 positive tumor cells. Conclusion The descending colon perivascular cell differentiation tumor is an undetermined biological behavior of mesenchymal tumors, with its unique imaging and histological features and immunohistochemical phenotypes. There is no clear diagnostic criteria for benign and malignant diseases. Surgical complete resection as the main treatment, follow-up after surgery.