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本文综合复习85例心脏淀粉样变,其中原发性心脏淀粉样变36例(第一组),心脏淀粉样变伴有神经肌肉淀粉样变8例(第二组),心脏淀粉样变伴血清球蛋白异常14例(第三组),老年性心脏淀粉样变27例(第四组)。第一组:36例中,男20例,女16例,均小于75岁(平均 56.7±3.5岁)。临床上91%患者有心力衰竭(其中左心衰竭55%,全心衰竭33%,右心衰竭
In this review, 85 cases of cardiac amyloidosis were reviewed. Among them, 36 cases were primary cardiac amyloidosis (group 1), 8 cases were cardiac amyloidosis with neuromuscular amyloidosis (group 2), cardiac amyloidosis Serum globulin abnormalities in 14 cases (third group), senile cardiac amyloidosis in 27 cases (fourth group). The first group: 36 cases, 20 males and 16 females, all less than 75 years (mean 56.7 ± 3.5 years). Clinically 91% of patients with heart failure (including 55% of left heart failure, heart failure 33%, right heart failure