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马凡氏综合征(以下简称本征),是一种先天性结缔组织异常的疾病其全身中胚叶组织广泛发育不良具有骨骼、眼及心血管三联征。现将我院所见一例报告如下: 马×,女,24岁,知青工。门诊号1533。4～5年来自觉劳累后心慌、乏力、气短。近两个月心前区呈阵发性针刺样疼痛,无放散,数分钟后便自行缓解。但平素从未介意,仍胜任一般体力劳动。笔者根据其体形异常,高度怀疑其为马凡氏综合征,特约患者于82年6月7日来院查体。患者自幼身体瘦长,手、足大,十二岁至十三岁发现双眼视力明显减退。十六岁时患胸膜炎(性质不详),曾于胸透时发现主动脉弓增宽。其家族无特殊。
Marfan syndrome (hereinafter referred to as the intrinsic), is a disease of congenital connective tissue abnormalities in its extensive mesodermal tissue with dysplasia skeletal, ocular and cardiovascular triad. Now we see a case of hospital reports are as follows: Ma ×, female, 24 years old, educated youth workers. Outpatient number 1533. 4 to 5 years after feeling tired tired, weakness, shortness of breath. Nearly two months precordial paroxysmal acupuncture-like pain, no discharge, a few minutes after they relieve themselves. But usually never mind, still qualified for general manual labor. According to the author of its anomalies, highly suspected of Marfan syndrome, special patients to June 7, 82 to the hospital examination. The patient grew thin, hands, feet large, 12-year-old to 13-year-old found that binocular vision decreased significantly. Pleuritis (unknown nature) at age sixteen was found to widen the aortic arch at chest radiography. No special family.