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由于胚胎发育上神经系统与皮肤均由外胚叶组织分化而来,因此外胚叶的发育异常可导致神经系统和皮肤同时出现病变,临床上常称为神经皮肤综合征(Neurocutaneus Syndrome).从广泛的意义来讲,该综合征包括先天性异常和后天性的一些疾病.其中有的以神经系统疾患为主伴有皮肤病变,有的以皮肤疾患为主,伴有神经系统病变.总之,神经系统和皮肤间存在着密切的关联,系统地瞭解其间的规律,有较为重要的临床意义,现作如下综述.先天性神经皮肤综合征一、母斑症(Neuroektodermose):母斑是先天性局限性皮肤色泽或表面形态的异常,生下即有或生后某个时期出现,一生中几乎不再改变的畸形.母斑症(Pharkomatoses)是皮肤和身体其它部位先天性畸形一组疾患的总称.
As the embryonic development of the nervous system and the skin are derived from the ectodermal tissue, so the development of ectodermal dysplasia can lead to nervous system and skin lesions at the same time, clinically often called neurocutaneous syndrome (Neurocutaneus Syndrome). From In a broad sense, the syndrome includes some diseases of congenital abnormalities and acquired diseases, some of which are characterized by neurodegenerative diseases and others with dermatological disorders and nervous system diseases.In short, There is a close relationship between the nervous system and the skin, a systematic understanding of the law during the more important clinical significance, are summarized as follows.Congenital neural skin syndrome, mother spot (Neuroektodermose): Mother spot is congenital Limited skin color or surface morphology abnormalities, birth that is, there is a certain period or postnatal period, almost no change in life deformities .Morphosis (Pharkomatoses) is a set of diseases of the skin and other parts of the body congenital malformations General