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近廿年来,陆续有预激综合征(W-P-W,Kent束型)呈家族性发生的报告,并提出家族性预激综合征是一种常染色体显性遗传性疾病。但对另一型预激综合征——L——G——L综合征呈家族性发生的报道还少见。作者发现一家父女二人皆有L-G-L综合征,并进一步对其全家三代共15人进行病史及心电图调查,共检出L-G-L综合征者7人,占该家系现有成员中的47％。(见家谱图)。资料患者(家系图Ⅰ_1)因高血病于1981年12月15日住院。体检:血压21/13kPa(160/100mmHg),心率64次/分。X线胸部后前位片示心肺正常,M超声心动图检查未见异常,心电图示L-G-L综合征,P-R间期0.10秒,QRS波群正常。经治疗后血压平稳出院。于1986年8月25日因排柏油样大便及呕吐咖啡
Nearly 20 years, one after another with pre-excitation syndrome (W-P-W, Kent bundle type) was a familial report and proposed familial WPW syndrome is an autosomal dominant genetic disease. However, there are few reports of familial occurrence of another type of WPW syndrome, L - G - L syndrome. The authors found that both father and daughter had L-G-L syndrome and further investigated the history and ECG of 15 people in their whole family for three generations. Seven L-G-L syndromes were detected, accounting for 47% of the existing members of the pedigree. (See family tree). Data patients (pedigree Figure I_1) were hospitalized for hyperlipidemia on December 15, 1981. Physical examination: blood pressure 21 / 13kPa (160 / 100mmHg), heart rate 64 beats / min. X-ray posterior chest film showed normal cardiopulmonary, M echocardiography showed no abnormal ECG L-G-L syndrome, P-R interval of 0.10 seconds, QRS wave group normal. After treatment, blood pressure was smoothly discharged. On August 25, 1986 due to Pai Pao like stool and vomit coffee