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地中海贫血因伴发自身免疫性溶血性贫血(AIHA)而造成急性溶血者较少见。我科1984～1994年收治5例,男2例,女3例,年龄4个月、6个月各1例,7～12岁3例,均为壮族。患儿自幼脸色苍白、乏力多汗,症状随年龄增长渐加重,本次均因脸色苍白突然加剧,皮肤黄染,尿浓茶样而入院,4例1周前有呼吸道感染史。1例输同型血时发生溶血反应。体检:发育营养均差,贫血貌,皮肤巩膜轻～中度黄疸,4例眼距增宽及鼻梁低平,肝脾不同程度肿大。血Hb43～73g/L,RBC1.48～2.75×10~(12)/L,网织红细胞0.025～0.18,尿潜血阳性5例,血清总胆红质及间接胆红质均升高;Hb电泳及抗碱试验,2例出现
Thalassemia is less common in patients with acute hemolysis due to autoimmune hemolytic anemia (AIHA). Our department from 1984 to 1994 admitted to 5 cases, 2 males and 3 females, aged 4 months, 6 months in 1 case, 7 to 12 years in 3 cases, are Zhuang. Children with pale face, fatigue, sweating, symptoms gradually aggravate with age, this are due to a sudden facial pale, yellow skin, urine tea samples and admission, 4 patients had a history of respiratory infection a week ago. Hemolytic reaction occurred in 1 case of transfusion of the same type of blood. Physical examination: development and nutrition were poor, anemic appearance, skin scleral mild to moderate jaundice, 4 cases of widening of the ocular distance and nasal low, liver and spleen to varying degrees. Blood Hb 43 ~ 73g / L, RBC 1.48 ~ 2.75 × 10 12 / L, reticulocyte 0.025 ~ 0.18, urine occult blood positive in 5 cases, serum total bilirubin and indirect bilirubin were increased; Hb electrophoresis And alkali resistance test, 2 cases appeared