慢性炎症性脱髓鞘性多发性神经病对自主神经系统的影响

• 作 者: Boukhris S. Magy L. 许刚
• 机 构: Service de Neurologie H.opital Universitaire Dupuytren 2 avenue Martin- Luther- King 87042 Limoges
• 出 处: 世界核心医学期刊文摘(神经病学分册)
• 发表日期: 2006年08期
• 关键词: 自主神经系统 侧胸部 静脉输注 右利手 报道提示 免疫调节 Claude 免疫球蛋白 综合征 病例

Introduction. Involvement of the autonomic nervous system during Chronic Inflammatory Demyelinating Polyneuropathy (CIDP) is rare. Localised hyperhydrosis and Claude Bernard Horner (CBH) syndrome have never been reported in patients with CIDP. Case report. We report the case of a 65- year- old right handed man who presented with hyperhydrosis localised to the right hemithorax and hemiface and a left CBH syndrome. After an extensive workup, the patient was found to have CIDP as the only cause of autonomic nervous system involvement. The symptoms resolved slowly after three courses of intravenous immunoglobulins. Conclusion. Signs of autonomic nervous system involvement can be observed in CIDP as in Guillain- Barré syndrome. This case report shows that immunomodulatory treatment can be effective against dysautonomia in CIDP.u001a

Introduction. Involvement of the autonomic nervous system during Chronic Inflammatory Demyelinating Polyneuropathy (CIDP) is rare. Localised hyperhydrosis and Claude Bernard Horner (CBH) syndrome have never been reported in patients with CIDP. Case report. We report the case of a 65- year - old right handed man who presented with hyperhydrosis localized to the right hemithorax and hemiface and a left CBH syndrome. After an extensive workup, the patient was found to have have CIDP as the only cause of autonomic nervous system involvement. The symptoms resolved slowly after three Signs of autonomic nervous system involvement can be observed in CIDP as in Guillain-Barré syndrome. This case report shows that immunomodulatory treatment can be effective against dysautonomia in CIDP. u001a