论文部分内容阅读
本文收集16例手术证实为双腔右心室(DCRV)畸形病例。手术见右室腔有异常肥大肌束引起流出道不同程度狭窄阻塞,其中13例形成肌膈膜中央有小孔,口径在0.4cm～1.5cm。狭窄部位较低,在流出道与流入道分界处,将右室分成近端高压与远端低压两个腔,低压腔较大,漏斗发育正常,无肺动脉狭窄。80%以上合并室缺。因此X 线平片表现多种多样。通常肺血减少,心腰不明显凹陷也不显著凸出,多为平直或略凸,多呈不典型主动脉型,不同法乐四联症和肺动脉瓣狭窄.心胸比值平均为0.51轻度增大或正常。右心室选择性造影可确诊,能显示右室腔内异常肌柬的形态、位置,又能观察到低压腔的大小及心内伴发其他畸形。
This article collected 16 cases of surgery confirmed double-chamber right ventricular (DCRV) deformity cases. Surgery see the right ventricular cavity abnormal muscle bundle caused by varying degrees of obstruction of the outflow tract obstruction, of which 13 cases of the formation of the diaphragm medial holes, diameter 0.4cm ~ 1.5cm. The narrow part of the lower part of the outflow tract and the inflow tract at the junction of the right ventricle is divided into two types of proximal and distal low pressure low pressure cavity larger, normal funnel development, no pulmonary stenosis. More than 80% of the combined vacancy. Therefore, a variety of X-ray film performance. Usually reduced pulmonary blood flow, obvious waist was not obvious convex bulge, mostly straight or slightly convex, mostly atypical aortic type, tetralogy of Fallot and different pulmonary valve stenosis. Increase or normal. Right ventricular selective radiography can be diagnosed, can show the right ventricular cavity abnormalities in the shape of the Cambodian, location, but also observed the size of the low-pressure cavity and the heart associated with other deformities.